Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease.
It is characterized by progressive cyst formation in both kidneys, often leading to end-stage kidney disease. Indications for surgical removal of an ADPKD kidney include intractable pain, hematuria, infection, or exceptional enlargement and small abdominal cavity hampering implantation of a donor kidney. We report the case of an extraordinarily large ADPKD kidney weighing 8.7 kg (19.3 lb) with a maximal length of 48 cm (19 inch), and with cysts filled with both clear and bloody fluid.
Written by:
Spithoven EM, Casteleijn NF, Berger P, Goldschmeding R. Are you the author?
Department of Nephrology, University Medical Center Groningen, University of Groningen, Groningen, The Netherlands; Department of Surgery, University Medical Center Utrecht, Utrecht, The Netherlands; Department of Pathology, University Medical Center Utrecht, Utrecht, The Netherlands.
Reference: Case Rep Nephrol Urol. 2014 Jun 4;4(2):109-12.
doi: 10.1159/000363378
PubMed Abstract
PMID: 25028584
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