Newborn with persistent cloaca presenting with accessory phallic urethra and ambiguous genitalia - Abstract

Division of Pediatric Urology, McMaster Children's Hospital, McMaster University, Hamilton, Ontario, Canada.

Persistent cloaca is a rare urogenital anomaly that can pose significant challenges for adequate diagnosis and management. We describe the case of an infant girl with a cloacal malformation, having a single perineal orifice and an accessory phallic urethra, who presented with ambiguous genitalia at birth. The distal part of the accessory phallic urethra was used to create a mucosa-lined vestibule as a part of the total urogenital sinus mobilization. This technical maneuver allowed a more natural looking, and possibly functioning, vaginal introitus, improving the final cosmetic result.

Written by:
Braga LH, Whelan K, Demaria J, Pippi-Salle JL.   Are you the author?

Reference: Urology. 2011 Feb 17. Epub ahead of print.
doi: 10.1016/j.urology.2010.12.044

PubMed Abstract
PMID: 21334047 Pediatric Urology Section