46 XY Denys-Drash Syndrome. Is There a Role for Nephron Sparing Modalities in Management of Renal Masses? A Report of Two Cases

Denys Drash Syndrome (DDS) is a combination of genital and urinary anomalies that mostly associated with renal and gonadal malignancies. We report 2 patients who presented with genital ambiguity and were diagnosed as 46XY DDS. Both patients had renal masses during follow up and underwent partial nephrectomy aiming to have transplant at older age.

Urology. 2018 Apr 30 [Epub ahead of print]

Amr Hodhod, Mohamed El-Sherbiny

Department of pediatric surgery; McGill University; The Montreal Children's Hospital, 1001 Boulevard Décarie, Montréal, QC, Canada, H4A 3J1. Electronic address: ., Department of pediatric surgery; McGill University; The Montreal Children's Hospital, 1001 Boulevard Décarie, Montréal, QC, Canada, H4A 3J1.